癫痫杂志

癫痫杂志

Rasmussen脑炎的研究进展

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Rasmussen脑炎(Rasmussen’s encephalitis,RE)是一种罕见的神经系统慢性疾病,又称为Rasmussen综合征。该病多起源于儿童期,常累及一侧大脑半球,主要以药物难治性癫痫、部分性癫痫持续状态、进展性神经功能缺损(言语、运动及认知功能障碍等)为主要特点。目前神经病理学及免疫学机制尚不明确。影像学检查对其早期诊断有指导意义。该病症状重,致残率高,抗癫痫药物治疗的疗效较差,激素及免疫抑制剂等药物治疗不能从根本上阻止疾病的进展,大脑半球切除术仍是目前唯一治愈该病的方法。

关键词: Rasmussen脑炎; 病因及发病机制; 临床表现; 诊断及治疗

引用本文: 黄亚莉, 任惠. Rasmussen脑炎的研究进展. 癫痫杂志, 2017, 3(3): 234-237. doi: 10.7507/2096-0247.20170036 复制

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